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NEJM 376:1668-1678, CASE 13-2017, 2017
Metabolic Disease and Stroke: MELAS
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Neurobrucellosis:Clinical and Neuroimaging Correlation
AJNR 25:395-401, Al-Sous,M.W.,et al, 2004
A Practical Approach to the Diagnosis and Management of MELAS: Case Report and Review
The Neurologist 8:302-312, Thambisetty,M.,et al, 2002
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Neurological Involvement in Wegener's Granulomatosis:An Analysis of 324 Consecutive Pts at the Mayo Clin
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Clinicopathologic Conference, Susacs Syndrome
NEJM 379:2152-2159, Case 37-2018, 2018
Sjogren Syndrome: Neurologic Complications
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Clinical Features: Outcome, and Meningococcal Genotype in 258 Adults With Meningococcal Meningitis: A Prospective Cohort Study
Medicine 87:185-192, Heckenberg,S.G.B.,et al., 2008
Community-Acquired Bacterial Meningitis in Adults
NEJM 354:44-53, van de Beek,D.,et al, 2006
Spontaneous Spinal Cerebrospinal Fluid Leaks and Intracranial Hypotension
JAMA 295:2286-2296, Schievink,W.I., 2006
Update on Susacs Syndrome
Curr Opin Neurol 18:311-314, Gross,M. &Eliashar,R., 2005
Susac Syndrome:Report of Four Cases and Review of the Literature
AJNR 25:382-388,351, Do,T.H.,et al, 2004
Sudden Unilateral Deafness Due to a Right Vertebral Artery Dissection
Neurol 62:1442, Raupp,S.F.A.,et al, 2004
Neurologic Manifestations in Primary Sjogren Syndrome: A Study of 82 Patients
Medicine 83:280-291, Delalande,S.,et al, 2004
Superficial Siderosis of the CNS Associated with Multiple Cavernous Malformations
AJNR 20:1245-1248, Whu,W.C.,et al, 1999
Retinocochleocerebral Vasculopathy
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Susac Syndrome
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Acute Vestibular Syndrome
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Chronic Progressive Panencephalitis due to Rubella Virus Simulating Subacute Sclerosing Panencephalitis
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Focusing on the Eye Signs of Alport Syndrome in a 40-Year-Old Man Who Previously Had a Kidney Transplant and Hearing Loss
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A 66-Year-Old Woman With Progressive Encephalopathy and Bilateral Hearing Loss
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Multiple Cranial Nerve Gadolinium Enhancement in Norrie Disease
Ann Neurol 91:158-159, Jokela, M.,et al, 2022
A 72-Year-Old Woman with Rapidly Progressive Bilateral Hearing Loss
Neurol 98:632-637, Alsalem, A.,et al, 2022
Bilateral Hearing Loss and Constricted Visual Fields
BMJ 378:e070672, Sachdeva, G. & Shafquat, S., 2022
Chronic Meningitis
NEJM 385:930-936, Aksamit, A.J., 2021
Clinical Reasoning: Siblings with Progressive Weakness, Hypotonia, Nystagmus, and Hearing Loss
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A Young Man with Progressive Vision and Hearing Loss
JAMA Neurol 73:880-883, Kung, N.H.,et al, 2016
Acoustic Apoplexy: An Acute Complication of a Common Intracranial Tumour
BMJ 348:g3268, Hollingworth, M.A.,et al, 2014
Intracranial Neoplasms and Paraneoplastic Disorders, Carcinomatous Meningitis
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Epilepsy, Ataxia, Sensorineural Deafness, Tubulopathy, and KCNJ10 Mutations
NEJM 360:1960-1970, Bockenhauer,D.,et al, 2009
Neurofibromatosis Type 2
Lancet 373:1974-1986, Astagiri,A.R.,et al, 2009
Neurologic Manifestations of von Hippel-Lindau Disease
JAMA 300:1334-1342, Butman,J.A.,et al, 2008
Superficial Siderosis
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Clinicopath Conf, Charcot-Marie-Tooth Disease Type 2, with Aides Pupil and a Mutation in MPZ Gene
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Mitochondrial DNA Polymerase-y and Human Disease
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Sensorineural Hearing Loss in Children
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Hearing Loss is a Common Feature of Symptomatic Children with Profound Biotinidase Deficiency
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Acute Bilateral Sensorineural Hearing Loss as the Presenting Symptom of Metastatic Lung Cancer
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Meningeal Carcinomatosis Manifested as Bilateral Progressive Sensorineural Hearing Loss
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Superficial Siderosis of the Central Nervous System,A Late Complication of Cerebellar Tumors
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Mild Traumatic Brain Injury,Toward Understanding Manifestations and Treatment
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Endolymphatic Sac Tumors, A Source of Morbid Hearing Loss in von Hippel-Lindau Disease
JAMA 277:1461-1466, Manski,T.J.,et al, 1997
Adult-Onset MELAS
Stroke 27:1420-1423, Gilchrist,J.M.,et al, 1996
Clinical and Genetic Abnormalities in Patients with Friedreich's Ataxia
NEJM 335:1169-1175, 12221996., Durr,A.,et al, 1996
Mitochondrial Neurogastrointestinal Encephalomyopathy (MMGIE) :Clin Biochem & Genetic Features of Auto Recess Mitochond Disorder
Neurol 44:721-727, Hirano,M.,et al, 1994
A Case of Tinnitus and Hearing Loss After Cerebellar Hemorrhage
Stroke 24:906-908, Matsuda,Y.,et al, 1993
The Pathogenesis of Superficial Siderosis of the Central Nervous System
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